Distal arthrogryposes are a group of syndromes with congenital contractures primarily
involving the hands and feet, which often are associated with abnormal facies, and are
transmitted by autosomal dominant inheritance. Many affected individuals present in an
orthopaedic setting. The features of these syndromes are described to allow diagnosis,
establish prognosis, provide family counseling, and treatment. Increased recognition will
lead to improved knowledge of the natural history.